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Gerstmann syndrome

A neurological disorder characterized by left-right disorientation, agraphia, acalculia, and finger agnosia, generally associated with lesions in the parietal lobe of the dominant cerebral ...

Gerstmann syndrome

Gerstmann syndrome n.   Quick reference

A Dictionary of Psychology (4 ed.)

Reference type:
Subject Reference
Current Version:
2015

... syndrome n . A neurological disorder characterized by left-right disorientation, agraphia , acalculia , and finger agnosia , generally associated with lesions in the parietal lobe of the dominant cerebral hemisphere. [Named after the Austrian neurologist Josef Gerstmann ( 1887–1969 ) who first noticed in 1930 the tendency for the four components of the syndrome to occur...

Gerstmann’s syndrome

Gerstmann’s syndrome   Quick reference

Concise Medical Dictionary (10 ed.)

Reference type:
Subject Reference
Current Version:
2020
Subject:
Medicine and health, Clinical Medicine
Length:
84 words

...’s syndrome a group of symptoms that represent a partial disintegration of the patient’s recognition of his or her body image . It consists of an inability to name the individual fingers, misidentification of the right and left sides of the body, and inability to write or make mathematical calculations ( see acalculia ; agraphia ). It is caused by disease in the association area of the dominant (usually left) parietal lobe of the brain. [ J. G. Gerstmann ( 1887–1969 ), Austrian neurologist...

Gerstmann–Straussler syndrome

Gerstmann–Straussler syndrome   Reference library

Oxford Dictionary of Biochemistry and Molecular Biology (2 ed.)

Reference type:
Subject Reference
Current Version:
2008
Subject:
Science and technology, Life Sciences
Length:
29 words

...–Straussler syndrome a transmissible spongiform encephalopathy of humans, usually familial, characterized by widespread degeneration of the nervous system. See also prion . [After Joseph Gerstmann ( 1887–1969 ), Austrian...

Gerstmann–Straussler–Scheinker syndrome

Gerstmann–Straussler–Scheinker syndrome   Quick reference

Concise Medical Dictionary (10 ed.)

Reference type:
Subject Reference
Current Version:
2020
Subject:
Medicine and health, Clinical Medicine
Length:
69 words

...–Straussler–Scheinker syndrome an autosomal dominant condition that is caused by a mutation in the prion protein gene and resembles Creutzfeldt-Jakob disease (CJD). Patients present with cerebellar dysfunction ( ataxia and dysarthria ) and later develop dementia. They continue to deteriorate over several years, in contrast with patients with CJD, who deteriorate rapidly over periods of less than 12 months. [ J. G. Gerstmann...

Gerstmann–Straussler–Scheinker syndrome

Gerstmann–Straussler–Scheinker syndrome   Quick reference

A Dictionary of Biomedicine (2 ed.)

Reference type:
Subject Reference
Current Version:
2019

...Gerstmann–Straussler–Scheinker syndrome A familial spongiform encephalopathy caused by mutation in the prion protein gene. Transgenic mice with the mutant form of the prion develop a degenerative brain disease similar, but not identical, to scrapie ....

Gerstmann–Sträussler–Scheinker syndrome

Gerstmann–Sträussler–Scheinker syndrome n.   Quick reference

A Dictionary of Psychology (4 ed.)

Reference type:
Subject Reference
Current Version:
2015

...–Sträussler–Scheinker syndrome n . A human prion disease usually regarded as a variant of Creutzfeldt–Jakob disease with pathology mainly in the cerebellum , leading to cerebellar syndrome . GSS abbrev . [Named after the Austrian neurologist Josef Gerstmann ( 1887–1969 ) and his colleagues Ernst Sträussler ( 1872–1959 ) and the Russian-born neuropathologist Ilya Mark Scheinker ( 1902–54 ) who first described its signs and symptoms in 1936...

Gerstmann–Straussler–Scheinker syndrome

Gerstmann–Straussler–Scheinker syndrome n.   Quick reference

A Dictionary of Nursing (8 ed.)

Reference type:
Subject Reference
Current Version:
2021
Subject:
Medicine and health
Length:
74 words

...–Straussler–Scheinker syndrome [ gerst -măn strows -ler shyn -ker] n. an autosomal dominant condition that is caused by a mutation in the prion protein gene and resembles Creutzfeldt-Jakob disease ( CJD ). Patients present with ataxia and dysarthria and later develop dementia. They continue to deteriorate over several years, in contrast with patients with CJD, who deteriorate rapidly over periods of less than 12 months. [ J. G. Gerstmann ( 1887–1969 ), Austrian...

Gerstmann syndrome

Gerstmann syndrome  

Reference type:
Overview Page
A neurological disorder characterized by left-right disorientation, agraphia, acalculia, and finger agnosia, generally associated with lesions in the parietal lobe of the dominant cerebral ...
Gerstmann-Straussler-Scheinker syndrome

Gerstmann-Straussler-Scheinker syndrome  

Reference type:
Overview Page
An autosomal dominant condition that is caused by a mutation in the prion protein gene and resembles Creutzfeldt-Jakob disease (CJD). Patients present with cerebellar dysfunction (ataxia and ...
cerebellar syndrome

cerebellar syndrome  

A pattern of signs and symptoms associated with damage to the cerebellum, including unsteady body movements, a characteristic cerebellar gait with feet wide apart and difficulty turning, ataxia, ...
acalculia

acalculia  

n. an acquired inability to make simple mathematical calculations. It is a symptom of disease in the dominant parietal lobe of the brain. See Gerstmann’s syndrome.
GSS

GSS  

Reference type:
Overview Page
1. Global Symptom Score.2. Glaucoma Staging System, for classifying visual field defects in glaucoma.3. See glutathione synthase.4. See Gerstmann–Straussler–Scheinker syndrome.5. The Genome Survey ...
prion disease

prion disease  

Any of a number of disorders of the nervous system, all fatal, believed to be caused by rogue prions, including scrapie in sheep, BSE in cattle, and the human prion diseases new-variant ...
finger agnosia

finger agnosia  

A form of autotopagnosia, usually associated with a lesion in the posterior region of the dominant hemisphere, characterized by a primary inability to recognize, identify, differentiate, name, ...
parietal lobe

parietal lobe  

The upper lobe on the side of each cerebral hemisphere, separated on its lateral or outer surface from the frontal lobe by the central sulcus, from the temporal lobe by the lateral sulcus and an ...
spongiform encephalopathy

spongiform encephalopathy  

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Overview Page
Any one of a group of rapidly progressive degenerative neurological diseases that include scrapie in sheep, bovine spongiform encephalopathy (BSE) in cattle, and kuru, Creutzfeldt-Jakob disease, and ...
encephalopathy

encephalopathy  

n. any of various diseases that affect the functioning of the brain. See hepatic encephalopathy, spongiform encephalopathy, Wernicke’s encephalopathy.
body image

body image  

Reference type:
Overview Page
(body schema) the individual’s concept of the disposition of his limbs and the identity of the different parts of his body. It is a function of the association areas of the brain. See also ...
scrapie

scrapie  

A spongiform encephalopathy of sheep. It is caused by a prion that produces progressive neurological deterioration, one symptom of which is to make the sheep scrape their fleece against posts, tree ...
agraphia

agraphia  

The loss of the ability to write, which may or may not be connected with alexia, the loss of ability to comprehend the written or printed word. It is thought ...

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